Rasmussen Encephalitis with Delayed Seizure Onset
نویسندگان
چکیده
منابع مشابه
Teaching NeuroImages: Radiographic progression in late-onset Rasmussen encephalitis.
A 20-year-old man presented who had epilepsy onset at age 15 with a single generalized tonic-clonic seizure, and after 2 years of seizure freedom, experienced emergence of dyscognitive and hypermotor seizures, and in the most recent 18 months, a progressive pattern of dyscognitive and focal motor complexand simple-partial status epilepticus involving the left extremities. EEG showed multifocal ...
متن کاملNeuropathological spectrum of Rasmussen encephalitis.
BACKGROUND Rasmussen encephalitis (RE) is a chronic epileptic disorder of unknown etiology, and is clinically characterized by progressive neurological deterioration, focal seizures often progressing to intractable epilepsy, cognitive decline and hemispheric atrophy. AIMS We report the spectrum of neuropathological changes seen in RE, and discuss the evolutionary mechanisms of this disease. ...
متن کاملUpregulation of Adenosine Kinase in Rasmussen Encephalitis
Rasmussen encephalitis (RE) is a rare neurologic disorder of childhood characterized by unihemispheric inflammation, progressive neurologic deficits, and intractable focal epilepsy. The pathogenesis of RE is still enigmatic. Adenosine is a key endogenous signaling molecule with anticonvulsive and anti-inflammatory effects, and our previous work demonstrated that dysfunction of the adenosine kin...
متن کاملRasmussen encephalitis: complementary role of multitechnique neuroimaging.
Rasmussen encephalitis is a chronic, progressive inflammation of the brain of unknown origin. Early diagnosis and treatment with immunoactive agents and/or hemispherectomy are sought to prevent the progressive cognitive decline that accompanies this disease. Combined anatomic and functional neuroimaging may serve to focus the diagnostic workup and to hasten brain biopsy for definitive diagnosis...
متن کاملPediatric anti-Hu–associated encephalitis with clinical features of Rasmussen encephalitis
Anti-Hu antibodies (anti-neuronal nuclear antibodies, type 1) are associated with paraneoplastic encephalomyelitis in adults, especially those with small cell lung cancer. Anti-Hu antibodies are extremely rare in children, but they have been observed in neuroblastoma with or without opsoclonus-myoclonus syndrome or in limbic encephalitis without associated malignancy. However, anti-Hu antibodie...
متن کاملذخیره در منابع من
با ذخیره ی این منبع در منابع من، دسترسی به آن را برای استفاده های بعدی آسان تر کنید
ژورنال
عنوان ژورنال: Pediatric Neurology Briefs
سال: 2004
ISSN: 2166-6482,1043-3155
DOI: 10.15844/pedneurbriefs-18-4-9